؟hlh disease

Description

https://www.hopkinsmedicine.org › health › conditions-and-diseases › hemophagocytic-lymphohistiocystosis

Hemophagocytic Lymphohistiocystosis | Johns Hopkins Medicine
https://www.hopkinsmedicine.org › health › conditions-and-diseases › hemophagocytic-lymphohistiocystosis
Treatment for familial or persistent acquired HLH may include: Chemotherapy (cancer drugs) Immunotherapy (drugs that affect your immune system) Steroids (drugs that fight inflammation) Antibiotic drugs Antiviral drugs

https://rarediseases.info.nih.gov › diseases › 6589 › hemophagocytic-lymphohistiocytosis

Familial hemophagocytic lymphohistiocytosis | Genetic and …
https://rarediseases.info.nih.gov › diseases › 6589 › hemophagocytic-lymphohistiocytosis
Hemophagocytic lymphohistiocytosis (HLH) is a condition in which the body makes too many activated immune cells (macrophages and lymphocytes). People with HLH usually develop symptoms within the first months or years of life.

https://www.chop.edu › conditions-diseases › hemophagocytic-lymphohistiocytosis-hlh

Hemophagocytic Lymphohistiocytosis (HLH) | Children’s …
https://www.chop.edu › conditions-diseases › hemophagocytic-lymphohistiocytosis-hlh
HLH is not a single disease. HLH is a group of rare disorders of the immune system. The immune system is the part of the body that fights infections. People with HLH become very ill, because the immune system doesn’t work properly. HLH can be caused by infections, cancer, or rheumatologic diseases.

https://primaryimmune.org › disease › hemophagocytic-lymphohistiocytosis-hlh

Hemophagocytic Lymphohistiocytosis (HLH) | Immune …
https://primaryimmune.org › disease › hemophagocytic-lymphohistiocytosis-hlh
Hemophagocytic lymphohistiocytosis (HLH) is a severe systemic inflammatory syndrome that can be fatal. This syndrome can sometimes occur in normal people with medical problems that can cause a strong activation of the immune system, such as infection or cancer. HLH in these settings is called Secondary HLH.

https://en.wikipedia.org › wiki › Hemophagocytic_lymphohistiocytosis

Hemophagocytic lymphohistiocytosis – Wikipedia
https://en.wikipedia.org › wiki › Hemophagocytic_lymphohistiocytosis
Hemophagocytic lymphohistiocytosis, also known as haemophagocytic lymphohistiocytosis, and hemophagocytic or haemophagocytic syndrome, is an uncommon hematologic disorder seen more often in children than in adults. It is a life-threatening disease of severe hyperinflammation caused by uncontrolled proliferation of activated lymphocytes and macrophages, characterised by proliferation of morphologically benign lymphocytes and macrophages that secrete high amounts of inflammatory cytokines. It is c

https://www.gosh.nhs.uk › conditions-and-treatments › conditions-we-treat-index-page-group › haemophagocytic-lymphohistiocytosis-hlh

Haemophagocytic lymphohistiocytosis (HLH) | Great Ormond …
https://www.gosh.nhs.uk › conditions-and-treatments › conditions-we-treat-index-page-group › haemophagocytic-lymphohistiocytosis-hlh
Haemophagocytic lymphohistiocytosis (HLH) Haemophagocytic lymphohistiocytosis (HLH) is a rare immune disorder where the body reacts inappropriately to a ‘trigger’, usually an infection. This page has been produced jointly between PID UK, Great Ormond Street Hospital (GOSH) and the Great North Children’s Hospital and in association with Histio UK.

https://www.urmc.rochester.edu › encyclopedia › content.aspx?ContentTypeID=134&ContentID=212

Acquired Hemophagocytic Lymphohistiocytosis (HLH) – Health …
https://www.urmc.rochester.edu › encyclopedia › content.aspx?ContentTypeID=134&ContentID=212
Hemophagocytic lymphohistiocytosis (HLH) is a rare immune system disease. It occurs more often in babies and young children. But it can also occur in adults. Children may inherit the disease through genes. This is called familial HLH. But in adults, many conditions can cause HLH. This is called acquired HLH.

https://www.cincinnatichildrens.org › service › h › hlh › about

What Is Hemophagocytic Lymphohistiocytosis | HLH Center of …
https://www.cincinnatichildrens.org › service › h › hlh › about
HLH stands for hemophagocytic lymphohistiocytosis. It is a life-threatening condition that can be defined as either primary or secondary HLH. Primary, or familial, HLH is when the condition is inherited. The term secondary HLH is used when your doctor thinks the condition may have occurred for a variety of other non-inherited reasons.

https://ashpublications.org › hematology › article › 2013 › 1 › 605 › 20850 › Hemophagocytic-lymphohistiocytosis-pathogenesis

Hemophagocytic lymphohistiocytosis: pathogenesis and …
https://ashpublications.org › hematology › article › 2013 › 1 › 605 › 20850 › Hemophagocytic-lymphohistiocytosis-pathogenesis
Hemophagocytic lymphohistiocytosis (HLH) is not an independent disease but rather a life-threatening clinical syndrome that occurs in many underlying conditions and in all age groups. HLH is the consequence of a severe, uncontrolled hyperinflammatory reaction that in most cases is triggered by an infectious agent.

https://ashpublications.org › hematology › article › 2015 › 1 › 190 › 20732 › Treatment-of-hemophagocytic-lymphohistiocytosis-in

Treatment of hemophagocytic lymphohistiocytosis in adults …
https://ashpublications.org › hematology › article › 2015 › 1 › 190 › 20732 › Treatment-of-hemophagocytic-lymphohistiocytosis-in
HLH is an orphan disease where close interaction with the national study centers is highly recommended. The registry initiative of the Histiocyte Society has the goal of collecting data on aHLH, which will allow the establishment of formal treatment guidelines derived from evidence and consensus.